Extensive mandibular multiloculation in a patient with Nevoid Basal Cell Carcinoma Syndrome: Case Report

Gorlin Goltz Syndrome, or Nevoid Basal Cell Carcinoma is an autosomal dominant genetic disease characterized especially by the manifestation of basal cell carcinomas in skin and keratocysts jaws. Additionally, patients may present with several other manifestations, such as bifid ribs, hypertelorism calcification falx cerebri. The diagnosis has physicians dentists protagonists investigation involves a good anamnesis associated detailed physical examination, imaging, anatomical histopathological exams and, if possible, identification PTCH1 gene, which covers approximately 85% patients. study aims to up-to-date integrative literary review highlighting care management case syndromic patient treated at stomatology clinic, carrying series major minor findings disease.